The coenzyme A thioester derivative of propionic acid; an intermediate in the degradation of l-valine, l-isoleucine, l-threonine, l-methionine, and odd-chain fatty acid s; a precursor for the synthesis of odd-chain fatty acid s; it accumulates in individuals with a deficiency of propionyl-CoA carboxylase.
- propionyl-CoA carboxylase an enzyme that catalyzes the reaction of propionyl-CoA with CO2 and ATP to produce ADP, orthophosphate, and d-methylmalonyl-CoA; a biotin-dependent enzyme; an inherited deficiency of this enzyme will lead to propionic acidemia and developmental retardation.

Medical dictionary. 2011.

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  • propionyl-CoA carboxylase — pro·pi·o·nyl CoA car·boxy·lase (proґpe ə nəl ko aґ kahr bokґsə lās) [EC] an enzyme of the ligase class that catalyzes the carboxylation of propionyl CoA to form methylmalonyl CoA; the reaction is part of the route by… …   Medical dictionary

  • Biotin-(propionyl-CoA-carboxylase (ATP-hydrolysing)) ligase — In enzymology, a biotin [propionyl CoA carboxylase (ATP hydrolysing)] ligase (EC number| is an enzyme that catalyzes the chemical reaction:ATP + biotin + apo [propionyl CoA:carbon dioxide ligase (ADP forming)] ightleftharpoons AMP +… …   Wikipedia

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  • propionyl — CH3CH2CO–; the acyl radical of propionic acid. SYN: propanoyl. * * * pro·pi·o·nyl prō pē ə .nil, .nēl n the monovalent radical C2H5CO of propionic acid * * * pro·pi·o·nyl (proґpe ə nəl) the acyl radical of propionic acid; the thioester… …   Medical dictionary

  • Ethylmalonyl-CoA-Weg — Der Ethylmalonyl CoA Weg ist ein Stoffwechselweg in Bakterien, der zur Assimilation von Acetat dient. Hierbei werden drei Moleküle Acetat, ein Molekül Kohlenstoffdioxid und ein Molekül Hydrogencarbonat zu den Citratzyklusitermediaten L Malat und… …   Deutsch Wikipedia

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