hydroxyproline oxidase

hy·droxy·pro·line ox·i·dase (hi-drok″se-proґlēn okґsĭ-dās) an enzyme of the oxidoreductase class that catalyzes the oxidation of 4-hydroxyproline to form the 3-hydroxy analog of Δ1-pyrroline 5-carboxylate as part of the pathway of degradation of free hydroxyproline. Deficiency of the enzyme, an autosomal recessive trait, results in hydroxyprolinemia.

Medical dictionary. 2011.

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  • hyperprolinemia — A metabolic disorder characterized by enhanced plasma proline concentrations and urinary excretion of proline, hydroxyproline, and glycine; autosomal recessive inheritance. Type I h. is associated with …   Medical dictionary

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